Rosai Dorfman disease - a rare cause of cervical lymphadenopathy.
Insiyah Amiji, Ummulkheir H. Mohamed, Hajaj Salum, Emilia Karugaba, Luka Lui, Livin Mumburi, Anna Msafiri, Higgins Massawe
Abstract
Rosai Dorfman disease is a rare cause of sinus histiocytosis with massive lymphadenopathy, in developing countries it mimics tuberculosis and malignancies like lymphoma and its often mismanaged. A high index of suspicion is necessary for its diagnosis. It resolves spontaneously therefore observation is currently the advocated approach for its management.
MeSH terms
- Sinus Histiocytosis with Massive Lymphadenopathy
- Rosai–Dorfman disease
- Medicine
- Cervical lymphadenopathy
- Disease
- Tuberculosis
- Lymphoma
- Rare disease
- Sinus (botany)
- Dermatology
- Histiocytosis
- Pathology