GRANULOMATOSIS WITH POLYANGIITIS MIMETIZING RHEUMATOID VASCULITIS
Rita Marina Soares de Castro Duarte, David Lopes Lima Cavalcanti Coelho, Caroline Diniz Bezerra, Alexsandro Paulo Costa Galdino, Leonardo Fernandes e Santana, Mateus de Sousa Rodrigues, Luana Barros Caxias de Souza, Bianca Alencar Dias de Almeida
Abstract
Granulomatosis with polyangiitis (GPA) is a pauci-immune necrotizing granulomatous vasculitis, which affects predominantly small vessels, mainly from the respiratory tract and kidneys. It has a broad spectrum of clinical manifestations that mimics other diseases, such as: Pyoderma gangrenosum, lymphoma, tuberculosis, sarcoidosis, subacute bacterial endocarditis and systemic lupus erythematosus. This case report aims to highlight the differential diagnosis of GPA with rheumatoid vasculitis.
MeSH terms
- Granulomatosis with polyangiitis
- Medicine
- Vasculitis
- Pyoderma gangrenosum
- Dermatology
- Sarcoidosis
- Differential diagnosis
- Necrotizing Vasculitis
- Tuberculosis
- Pathology
- Polyarteritis nodosa